Dermatomyositis

Case contributed by Yaïr Glick , 10 Jun 2019
Diagnosis certain
Changed by Dalia Ibrahim, 12 Jun 2019

Updates to Study Attributes

Findings was changed:

CT neck-chest-abdomen obtained several months previously

Coarse subcutaneous calcifications in the arms, chest wall and abdominal wall (Calcinosis universalis).Very little intramuscular calcification, notably in the quadratus femoris muscles.

Updates to Case Attributes

Body was added:

Calcinosis universalis is a condition characterised by long bands or sheets of symmetrical subcutaneous calcification.

~1/3 of cases are associated with sclerodermadermatomyositis, polymyositis, and systemic lupus erythematosus.

Calcinosis universalis manifests as long bands of symmetrical subcutaneous calcification seen extending along deep fascial planes. Tendon and ligamental involvement has been described.

Unlike tumoural calcinosis, it is plaque or sheet like rather than mass like.

  • +<p><a title="Calcinosis universalis" href="/articles/calcinosis-universalis"><strong>Calcinosis universalis</strong></a> is a condition characterised by long bands or sheets of symmetrical subcutaneous calcification.</p><p>~1/3 of cases are associated with <a href="/articles/scleroderma">scleroderma</a>, <a href="/articles/dermatomyositis">dermatomyositis</a>, <a href="/articles/polymyositis">polymyositis</a>, and <a href="/articles/systemic-lupus-erythematosus">systemic lupus erythematosus</a>.</p><p>Calcinosis universalis manifests as long bands of symmetrical subcutaneous calcification seen extending along deep fascial planes. Tendon and ligamental involvement has been described.</p><p>Unlike <a href="/articles/tumoral-calcinosis">tumoural calcinosis</a>, it is plaque or sheet like rather than mass like.</p>

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