Diastematomyelia

Case contributed by Dr Praveen Jha

Presentation

Scoliotic deformity since birth. Hair tuft in back.

Patient Data

Age: 10
Gender: Male
MRI

Spinal cord separated into two halves by a bony spur as described, and seen on coronal and axial images.

Case Discussion

A 10 year old male presented with scoliotic deformity since birth, with a hairy skin tag in his back. Multiple segmentation anomalies were observed on plain radiograph, with widening of interpedicular distance. MRI was subsequently performed to evaluate status of spinal cord.

T2 sagittal images reveal spinal cord split into two halves from the level of lower dorsal vertebra up to S1 vertebra. T1 and T2 axial images show spinal cord split into two halves, with a hypointense (on both T1/T2) spur in the midline. Each hemicord is enclosed within its own dural sheath, and bony/fibrous spur was found between these sacs. An associated 'dermal sinus' can also be seen with dysraphic spine and vertebral segmentation anomalies.

A diagnosis of Pang Type 1 diastematomyelia was made.

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Case information

rID: 9493
Case created: 24th Apr 2010
Last edited: 3rd Jun 2017
Inclusion in quiz mode: Included

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