Diffuse abdominal plexiform neurofibromatosis

Case contributed by Dr Amr Farouk

Presentation

6 years old patient with abdominal pain and increasing abdominal girth.

Patient Data

Age: 6 years

Multiple solid fusiform masses along the distribution of nerves infiltrating throughout the hepatic hilum, small bowel mesentery and greater omentum. They are seen showing homogenous low attenuation.

Right femoral nerve thickening is noted as well.

Case Discussion

Pathologically proven diffuse abdominal and retroperitoneal plexiform neurofibromatosis.

PlayAdd to Share

Case information

rID: 44418
Case created: 20th Apr 2016
Last edited: 2nd Jun 2016
Inclusion in quiz mode: Included

Updating… Please wait.
Loadinganimation

Alert accept

Error Unable to process the form. Check for errors and try again.

Alert accept Thank you for updating your details.