Double outlet right ventricle (with VSD and PAH)
recurrent dyspnea since birth. Prior ECHO reveals pulmonary arterial hypertension and ventricular septal defect.
Loading Stack -
0 images remaining
Aorta and pulmonary artery are seen to arise from right ventricle, with a large ventricular septal defect in the membranous ventricular septum, with partial AV canal defect. Markedly dilated pulmonary artery is seen suggesting pulmonary arterial hypertension.
This is a characteristic case of Double outlet right ventricle.
This patient was taken for surgery, and diagnosis was confirmed. However, patient died intra-operatively probably due to severe concurrent PAH.