Dyke-Davidoff-Mason syndrome

Case contributed by Dr Bruno Di Muzio

Presentation

Long history of well-controlled epilepsy. Two recent seizures.

Patient Data

Age: 70-year-old
Gender: Female
MRI

MRI Brain (selected images)

These select sequences demonstrate an atrophic right hemisphere, with prominently ex vacuo dilated right lateral ventricle and gliosis/periventricular FLAIR hyperintensity. In addition, there is compensatory bony changes, with a large right frontal sinus, as well as right sided calvarial thickening and elevated petrous ridge. The falx is also deviated to the right.

The remainder study (not shown) is unremarkable. 

Case Discussion

This brain MRI demonstrates findings in keeping with Dyke-Davidoff-Mason syndrome: atrophy or hypoplasia of one cerebral hemisphere (hemiatrophy). In radiology, this so-called syndrome is more likely to represent a group of radiological findings that expresses a possible sequela of a fetal or early childhood period brain insult

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Case information

rID: 42787
Case created: 8th Feb 2016
Last edited: 9th Feb 2016
Tag: rmh
Inclusion in quiz mode: Included

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