Dyke Davidoff Mason syndrome with crossed cerebellar diaschisis

Case contributed by Dr Iqbal Naseem

Presentation

Patient presented with recent onset of seizures.

Patient Data

Gender: Male

CT images showing left cerebral and right cerebellar atrophy.

Also noted is left sided increased calvarial thickness. 

Case Discussion

Dyke Davidoff Mason syndrome is characterized by unilateral cerebral hemiatrophy associated with ipsilateral increased bony thickness and enlarged paranasal sinuses. Etiology being vascular insult during intranatal period.

Sometimes this syndrome is associated with contralateral cerebellar hemiatrophy known as crossed cerebellar diaschisis. 

PlayAdd to Share

Case information

rID: 19627
Case created: 29th Sep 2012
Last edited: 5th Feb 2016
Inclusion in quiz mode: Included

Updating… Please wait.
Loadinganimation

Alert accept

Error Unable to process the form. Check for errors and try again.

Alert accept Thank you for updating your details.