Citation, DOI & case data
History of left hemiplegia since the age of 4 months with right hemiparesis.
Loading Stack -
0 images remaining
The MRI sequences demonstrate:
- atrophy of the right cerebral hemisphere with temporofrontal cystic encephalomalacia, surrounding gliosis and ex-vacuo dilatation of the right lateral ventricle
- compensatory thickening of the ipsilateral skull vault
- moderate enlargement of the ipsilateral sphenoid sinus and mastoid air-cells
The MRI features most consistent with Dyke-Davidoff-Masson syndrome with right cerebral hemiatrophy, cystic encephalomalacia with surrounding gliosis and compensatory thickening of the calvarium.
Dyke-Davidoff-Masson syndrome refers to hemicerebral atrophy/hypoplasia secondary to brain insult usually in the fetal or early childhood period and characterized by ipsilateral compensatory hypertrophy of the skull vault and contralateral hemiparesis.