Presentation
The patient has been suffering from fits since childhood, followed by right-sided weakness.
Patient Data
There is marked atrophy of the left cerebral hemisphere with evidence of fronto-parietal cystic encephalomalacia and ex-vacuo dilatation of the ipsilateral lateral ventricle.
Remodeling of the overlying calvarium is seen in left side.
The right-sided cerebral hemisphere is grossly unremarkable.
Note, however, that the images have not been obtained in the true axial plane but rather significantly tilted. This markedly accentuates the apparent asymmetry of the skull vault.
Case Discussion
CT findings are most likely suggestive of Dyke-Davidoff-Masson syndrome, as described above, although the positioning of this scan makes this much harder to confirm.
Co-contributor: Dr. Anwar-ul-Haq Zadran.