Dysembroplastic neuroectodermal tumors (DNET's): bilateral

Case contributed by Dr Amr Farouk

Presentation

Recurrent seizures.

Patient Data

Age: 16 years
Gender: Female

Two right frontal and left temporal cortical lesions are seen measuring about 2 x 1.5 x 1.2 cm and 2.2 x 1.6 x 1.5 cm at their maximal axial and craniocaudal dimensions respectively. The lesions show high signal 'bubbly appearance' on T2 WIs, low signal on T1 WIs. The lesions exert minimal mass effect on the nearby cortical sulci, and on the left there is also scallop the inner table of of the skull vault.

Case Discussion

Cortical with hardly any surrounding vasogenic edema and bubbly appearance on T2 WIs are imaging findings suggestive of dysembryoplastic neuroectodermal tumors (DNET).  The main differential is that of multinodular and vacuolating neuronal tumors (MVNT)

Unfortunately, no histology or followup is available. 

This case illustrates bilateral cortical lesions that favor DNETs (presumptive diagnosis). Multifocality of DNET is rare and has already been described in the medical literature. 

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Case information

rID: 39043
Published: 17th Aug 2015
Last edited: 30th May 2019
Inclusion in quiz mode: Excluded

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