Dysembryoplastic neuroepithelial tumor (DNET)

Case contributed by Dr Akos Jaray

Presentation

Treatment resistant focal epilepsy. EEG shows left temporo-parieto-occipital focus. MRI to rule out structural cause.

Patient Data

Age: 10 years
Gender: Male

High T2 weighted signal intensity lesion (3 x 2 cm) within the left parietal region which only part suppresses on the fluid attenuated sequences.

Although peripherally placed, majority of this lesion is in a subcortical position likely to be involving the deeper cortex.
There is some minor mass effect as evidenced by adjacent sulcal effacement.

Bright rim sign is noted on FLAIR images.

No other epileptogenic foci present.

There is no evidence of contrast enhancement and there is no restriction of diffusion here. 

 

Case Discussion

Typical story of longstanding, treatment-resistant seizures.

Unfortunately the bright rim sign on FLAIR images may appear in low-grade astrocytoma as well.

Histology approved DNET.

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Case information

rID: 74893
Published: 8th Mar 2020
Last edited: 8th Mar 2020
Inclusion in quiz mode: Included
Institution: University of Pécs

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