Dysplastic cerebellar gangliocytoma
36-year-old female with a history of sinonasal inverted papilloma and incidental cerebellar lesion on CT-scan.
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T2/FLAIR hyperintense lesion in the left cerebellar hemisphere showing two components: a very T2 hyperintense rounded area with well defined margins and a more medial ill defined area of hyperintensity. The lesion shows no enhancement after contrast administration.
The lesion was surgically removed and the presence of Lhermitte-Duclos disease (dysplastic cerebellar gangliocytoma) was confirmed by pathology. This lesion has a very atypical appearance without the classic features of dysplastic cerebellar gangliocytoma consisting of widened cerebellar folia and striated pattern.
- Nowak DA, Trost HA. Lhermitte-Duclos disease (dysplastic cerebellar gangliocytoma): a malformation, hamartoma or neoplasm?. (2002) Acta neurologica Scandinavica. 105 (3): 137-45. Pubmed