Dysplastic cerebellar gangliocytoma

Case contributed by Paula Alcaide Leon

Presentation

36-year-old female with a history of sinonasal inverted papilloma and incidental cerebellar lesion on CT-scan.

Patient Data

Age: 36
Gender: Female

T2/FLAIR hyperintense lesion in the left cerebellar hemisphere showing two components: a very T2 hyperintense rounded area with well defined margins and a more medial ill defined area of hyperintensity. The lesion shows no enhancement after contrast administration.

Case Discussion

The lesion was surgically removed and the presence of Lhermitte-Duclos disease (dysplastic cerebellar gangliocytoma) was confirmed by pathology. This lesion has a very atypical appearance without the classic features of dysplastic cerebellar gangliocytoma consisting of widened cerebellar folia and striated pattern.

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Case information

rID: 58304
Published: 11th Feb 2018
Last edited: 11th Feb 2018
Inclusion in quiz mode: Included
Institution: St Michael's Hospital, Toronto

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