Dysplastic gangliocytoma of the cerebellum (Lhermitte-Duclos disease)

Case contributed by Dr Alessandro Spano Mello

Presentation

Female, headache and ataxia.

Patient Data

Age: 35
Gender: Female

Expansive lesion at right cerebellar hemisphere and vermis, hyperintense in T2, isointense in T1, without enhancement or restricted diffusion in DWI (but shows T2 shine through effect), with mass effect and fourth ventricle shift and effacement.

 

Case Discussion

MRI of a 35 woman with dysplastic gangliocytoma of the cerebellum (Lhermitte-Duclos disease), that is a rare posterior fossa disease that results in a cerebellar expansive appearance and thickened folia. The lesion is isointense in T1 and hyperintense in T2, without enhancement. There is a posterior fossa mass effect with fourth ventricle shift and effacement.  A ventricular diversion was performed before the MRI scan. 

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Case information

rID: 32289
Case created: 23rd Nov 2014
Last edited: 30th Jan 2016
Inclusion in quiz mode: Included

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