Ebstein anomaly

Case contributed by Vincent Tatco

Presentation

History of progressive exertional dyspnea and episodes of cyanosis. Physical examination revealed a murmur. Electrocardiography demonstrated right bundle-branch block.

Patient Data

Age: 10 years
Gender: Female
x_ray

There is marked cardiomegaly with a huge right atrial margin and somewhat squared or box-shaped appearance. 

The aorta and main pulmonary artery segment are not well delineated. 

The visualized pulmonary vascularity is within normal to slightly decreased.  

Annotated image

Annotated image showing the box-shaped heart.

Author: Vincent Tatco

License: CC-NC-BY-SA

Case Discussion

This case shows the radiographic appearance of the cardiac silhouette in an echocardiographically proven Ebstein anomaly.

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