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well defined lytic lesion in the mid to distal aspect of the proximal phalanx of the index finger. No cortical breach and no periosteal reaction. No fracture can be seen. No other lesions. No soft tissue calcification.
Enchondroma is a benign cartilaginous neoplasm in the medullary cavity. Most echondromas are
asymptomatic but may present as pathological fractures. Peak age is 10-30 years.
- Tubular bones (hand, foot): 50%
- Femur, tibia, humerus
- Lytic lesion in bones of the hand or foot
- Chondroid calcifications: rings and arcs pattern ("O" and "C")
- Scalloped endosteum
- Expansion of cortex but no cortical breakthrough unless fractured
- No periosteal reaction or soft tissue mass
- In the absence of a fracture, a painful enchondroma is considered malignant until proven otherwise.
- Malignant transformation occurs but is rare.
Enchondromatosis (Ollier disease)
Ollier disease is a nonhereditary abnormality in which multiple enchondromas are present. Many lesions become stable at puberty. Risk of malignant transformation to chondrosarcoma is 25%.
- Multiple radiolucent expansile masses in hand and feet
- Hand and foot deformity
- Tendency for unilaterality
Maffucci syndrome comprises enchondromatosis and multiple soft tissue hemangiomas. Unilateral involvement of hands and feet. Malignant transformation is much more common than in Ollier's disease.