Endolymphatic sac tumor
Updates to Case Attributes
Patient with von Hippel Lindau-Lindau syndrome (vHL) and had previously underwent resection ofresected a left cerebellar hemangioblastoma (signs of cranioplasty on CT).
These studies show a mass mass in retrolabyrinthineretro labyrinthine portion of the right temporal bone, involving part part of jugular foramen,that that was confimedconfirmed as a an endolymphatic sac tumortumour. This tumor, which occurs in about 16% of patients with von Hippel-Lindau syndrome syndrome.
This patient also has an MRI study of the abdomen that showsshowing another vHL common feature: multiple renal cysts.
-<p>Patient with <a href="/articles/von-hippel-lindau-disease-5">von Hippel Lindau syndrome (vHL)</a> and had previously underwent resection of a left <a href="/articles/haemangioblastoma-central-nervous-system">cerebellar hemangioblastoma</a>.</p><p>These studies show a mass in retrolabyrinthine portion of the right temporal bone,<span style="line-height:1.6em"> involving part of jugular foramen, </span><span style="line-height:1.6em">that was confimed as a </span><a style="line-height: 1.6em;" href="/articles/endolymphatic-sac-tumour">endolymphatic sac tumor</a><span style="line-height:1.6em">. This tumor occurs in about 16% of patients with von Hippel-Lindau syndrome.</span></p><p>This patient also has an MRI study of abdomen that shows another vHL common feature: multiple renal cysts.</p><p> </p>- +<p>Patient with <a href="/articles/von-hippel-lindau-disease-5">von Hippel-Lindau syndrome (vHL)</a> and had previously resected a left <a href="/articles/haemangioblastoma-central-nervous-system-1">cerebellar hemangioblastoma</a> (signs of cranioplasty on CT).</p><p>These studies show a mass in retro labyrinthine portion of the right temporal bone, involving part of jugular foramen, that was confirmed as an <a href="/articles/endolymphatic-sac-tumour">endolymphatic sac tumour</a>, which occurs in about 16% of patients with von Hippel-Lindau syndrome.</p><p>This patient also has an MRI study of the abdomen showing another vHL feature: multiple renal cysts.</p>
Updates to Study Attributes
Mass that erodes and invades the posterior wall of petrous part of the right temporal bone (retrolabyrinthine(retro labyrinthine portion of the temporal bone), involving part part of the jugular foramen.
Updates to Study Attributes
Mass eroding and invading the retrolabyrinthine the retro labyrinthine portion of therighttemporal bone.
Extra-axial lesion without promoting thrombosis of the venous sinuses.
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