Posterior fossa ependymoma

Case contributed by Vincent Tatco
Diagnosis almost certain

Presentation

Known case of fourth ventricular tumor. For further evaluation prior to excision.

Patient Data

Age: 5 years
Gender: Male
mri

There is a lobulated mass within and expanding the fourth ventricle. The mass is isointense to the adjacent cerebellum on T1-weighted images and hyperintense on T2-weighted images. No evidence of hemorrhage or calcification is identified. After contrast infusion, vessels run through the mass with small, rounded, peripherally enhancing nodules within and just superior to the mass near the tectum. The cerebellum is effaced peripherally and the brainstem anteriorly. The mass extends anteriorly into the right foramen of Luschka as well as into the foramen of Magendie inferiorly, down to the upper cervical space dorsally.

A shunt catheter is seen in the right posterior parietal region coursing centrally with its tip just beyond the left leaflet of the cavum septum vergae. The lateral and third ventricles are dilated reflective of hydrocephalus.

Case Discussion

This case demonstrates the imaging features of a posterior fossa ependymoma. The patient underwent posterior fossa craniotomy and resection of the tumor. Histopathology confirmed the diagnosis of conventional ependymoma (WHO grade 2).

Note: as molecular profiling is unavailable in this case, it would have the diagnosis of posterior fossa ependymoma not otherwise specified (NOS). 

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