Erdheim-Chester disease

Case contributed by A.Prof Frank Gaillard

MRI through the orbits and posterior fossa demonstrates masses involving the intraconal compartment of the orbits and the extraaxial compartment posterior to the cerebellum. These masses are isointense to brain on T1 weighted images, and of marked low signal on T2. Enhancement is present following contrast administration.

Case Discussion

Features are consistent with Erdheim-Chester Disease, subsequently histologically proven. 

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Case information

rID: 2591
Published: 7th May 2008
Last edited: 16th Jul 2018
Tag: orbit
Inclusion in quiz mode: Included

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