Erdheim-Chester disease

Case contributed by Dr Andrew Lawson

Presentation

Abdominal pain

Patient Data

Age: 60
Gender: Male
Modality: CT

The liver is normal in size and density. No focal hepatic lesion. Gallbladder unremarkable. No dilatation of the biliary tree. There is a thin rim of hypodensity around the pancreas.

Extensive retroperitoneal soft tissue density surrounding both adrenals, kidneys, ureters, lower abdominal vasculature and pelvic vasculature, bladder  and prostate is similar compared to April 2104. Left JJ stent in situ. 

Generalised stranding of the mesentery. Mild stranding associated with the ascending colon.

Impression:

Soft tissue encasing the majority of the retroperitoneal structures consistent with the known diagnosis of Erdheim Chester disease. 

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Case Information

rID: 29803
Case created: 24th Jun 2014
Last edited: 28th Sep 2016
Inclusion in quiz mode: Included

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