Erdheim-Chester disease

Case contributed by Dr Andrew Lawson

Presentation

Abdominal pain

Patient Data

Age: 60 years
Gender: Male
CT

The liver is normal in size and density. No focal hepatic lesion. The gallbladder is unremarkable. No dilatation of the biliary tree. There is a thin rim of hypodensity around the pancreas.

Extensive retroperitoneal soft tissue density surrounding both adrenals, kidneys, ureters, lower abdominal vasculature and pelvic vasculature, bladder and prostate. Left DJ stent in situ. 

Generalized stranding of the mesentery. Mild stranding associated with the ascending colon.

Impression:

Soft tissue encasing the majority of the retroperitoneal structures consistent with the known diagnosis of Erdheim Chester disease. 

PlayAdd to Share

Case information

rID: 29803
Published: 25th Jun 2014
Last edited: 14th Aug 2019
Inclusion in quiz mode: Included

Updating… Please wait.

 Unable to process the form. Check for errors and try again.

 Thank you for updating your details.