Extra-abdominal desmoid fibromatosis

Case contributed by Domenico Nicoletti
Diagnosis certain

Presentation

About six month history of swelling over the right side of neck. No history of trauma.

Patient Data

Age: 25 years
Gender: Female

MRI chest with contrast

Mass of the upper margin of the right trapezius muscle, oval-shaped, of regular contours, well defined, intense enhanced after Gadolinium injection. There are no pathological adenopathies.

pathology

Histological report (in Italian),

Case Discussion

Aggressive fibromatosis is a benign fibrous neoplasm arising from fascia, periosteum and musculoaponeurotic structures of the body with no metastatic potential resulting from the abnormal infiltrating proliferation of fibroblasts. In the head and neck region, fibromatosis tends to be locally aggressive and to invade bone and soft tissue structures. Three types of these tumors can be distinguished: intra-abdominal form, the form of the abdominal wall, and extra-abdominal form. Histologically, desmoids are characterized by the proliferation of uniform spindle cells resembling myofibroblasts, in a background of abundant collagenous stroma and vascular network.

Radiographer: TSRM Fabio Imola

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