Fahr syndrome

Case contributed by Dr Mohammad Nawaz Nasery

Presentation

Headache and seizure.

Patient Data

Age: 25 years
Gender: Male
CT

Extensive dense calcifications in the basal ganglia bilaterally, most significantly in the caudate and lentiform nuclei, as well as in the white matter supra- and infratentorially.

Case Discussion

Fahr syndrome is characterized by calcification of the basal ganglia and white matter with subsequent neuronal loss. It classified as either primary, known as primary familial brain calcification, or secondary, due to underlying metabolic, infectious and traumatic causes. The usual age of onset is between 40-50 years, and clinically the syndrome may be asymptomatic or present with a variety of neurological and psychiatric manifestations.

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Case information

rID: 68217
Published: 20th May 2019
Last edited: 22nd May 2019
Inclusion in quiz mode: Included
Institution: Kabul medical university Ali Abad teaching hospital

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