Fahr syndrome

Case contributed by Dr Danilo Ferreira Maia


16-years-old male patient presenting with headache and vomiting 12 years after excision of medulloblastoma.

Patient Data

Age: 16 years
Gender: Male

CT Brain

Extensive symmetric calcifications involving caudate, lentiform nucleus, thalamus, and subcortical white matter.

Case Discussion

Fahr syndrome, also called estriatopalidodendate calcinosis, is characterized by extensive calcification of the base ganglia, dentate nucleus, thalamus, and subcortical white matter. It may be primary, familial, or secondary, such as HIV, hypoparathyroidism, hyperparathyroidism, sequelae of chemotherapy or radiotherapy, among others.

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Case information

rID: 66379
Published: 4th Mar 2019
Last edited: 14th Aug 2019
Inclusion in quiz mode: Excluded
Institution: Santa Casa de Belo Horizonte

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