Fibrous dysplasia of the orbital roof

Case contributed by Dr Abdel-Rahman Abdel-Halim

Presentation

Facial deformity in a teenager.

Patient Data

Age: 16
Gender: Male
Modality: CT

Axial CT images of the skull (bone window) revealed an expansile bone lesion with a typical ground glass appearance involving the roof of the right orbit.

Note the mass effect on the ipsilateral frontal sinus and right orbit.

Case Discussion

  • Fibrous dysplasia is a developmental anomaly manifested as a defect in osteoblastic differentiation and maturation.
  • It can affect any bone of the body.
  • The skull and facial bones are the affected sites in 10–25% of patients with monostotic fibrous dysplasia and in 50% of patients with polyostotic fibrous dysplasia. 

CT radiological features have three varities:

  1. Ground glass pattern (more than 50 %): as in this case.
  2. Homogeneously dense pattern (about 25%).
  3. Cystic pattern (about 20 %). 
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Case Information

rID: 41518
Case created: 5th Dec 2015
Last edited: 6th Apr 2017
Inclusion in quiz mode: Included

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