Fontan circulation
Updates to Case Attributes
History of tricuspid atresia type IA status post right-sided cavopulmonary anastomosis, extracardiac Fontan, and left pulmonary artery stent placement.
The initial VQ scan performed with a right upper extremity IV line demonstrates a complete lack of perfusion to the left lung and normal ventilation imaging. The right-sided cavopulmonary anastomosis allows passive venous return to the pulmonary arteries. Unilateral flow to the right pulmonary artery may be seen, as in this case, mimicking a pulmonary embolism on perfusion scan. The extracardiac conduit allows flow from the IVC to both pulmonary arteries without the mechanical help of the right ventricle. Repeat perfusion images following pedal injection showed homogeneous perfusion to both lungs.
Case prepared with the help of Dr. Suzanne Parets and Dr. SamSamuel Valle.
-<p>History of tricuspid atresia type IA status post right-sided cavopulmonary anastomosis, extracardiac Fontan and left pulmonary artery stent placement. </p><p>The initial VQ scan performed with a right upper extremity IV line demonstrates a complete lack of perfusion to the left lung and normal ventilation imaging. The right-sided cavopulmonary anastomosis allows passive venous return to the pulmonary arteries. Unilateral flow to the right pulmonary artery may be seen, as in this case, mimicking a pulmonary embolism on perfusion scan. The extracardiac conduit allows flow from the IVC to both pulmonary arteries without the mechanical help of the right ventricle. Repeat perfusion images following pedal injection showed homogeneous perfusion to both lungs.</p><p>Case prepared with the help of Dr. Suzanne Parets and Dr. Sam Valle.</p>- +<p>History of <a title="Tricuspid atresia" href="/articles/tricuspid-atresia">tricuspid atresia</a> type IA status post right-sided cavopulmonary anastomosis, extracardiac <a title="Fontan procedure" href="/articles/fontan-procedure">Fontan</a>, and left pulmonary artery stent placement. </p><p>The initial <a title="VQ scan" href="/articles/vq-scan-2">VQ scan</a> performed with a right upper extremity IV line demonstrates a complete lack of perfusion to the left lung and normal ventilation imaging. The right-sided cavopulmonary anastomosis allows passive venous return to the pulmonary arteries. Unilateral flow to the right <a title="Pulmonary artery" href="/articles/pulmonary-trunk">pulmonary artery</a> may be seen, as in this case, mimicking a pulmonary embolism on perfusion scan. The extracardiac conduit allows flow from the IVC to both pulmonary arteries without the mechanical help of the right ventricle. Repeat perfusion images following pedal injection showed homogeneous perfusion to both lungs.</p><p>Case prepared with the help of Dr. Suzanne Parets and Dr. Samuel Valle.</p>