Frontoethmoidal meningoencephalocele: nasofrontal type

Case contributed by Dr Pradosh Kumar Sarangi

Presentation

Swelling at the root of nose since birth, which is shown to be expansive on the Valsalva manoeuvre.

Patient Data

Age: 10-month-old
Gender: Female

There is an herniation of brain matter (frontal lobe) along with meninges through a midline defect in the frontoethmoidal bone. The swelling lies externally between frontal bone and nasal bone. There is no communication with the ventricles. The remainder brain parenchyma appears normal.

Case Discussion

This case typically illustrates a frontoethmoidal meningoencephalocele. There is herniation of brain matter (frontal lobe) along with meninges through a defect in frontoethmoidal bone. The swelling lies externally between frontal bone and nasal bone leading to nasofrontal type of meningoencephalocele.

Other two types of frontoethmoidal encephaloceles are nasoethmoidal, which exits between the nasal bone and nasal cartilages and naso-orbital, which exits through a defect in the maxillary frontal process. Frontoethmoidal encephaloceles are also known as sincipital encephaloceles.

 

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Case information

rID: 41623
Case created: 10th Dec 2015
Last edited: 3rd Jul 2017
Inclusion in quiz mode: Included

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