Presentation
Swelling at the root of nose since birth, which is shown to be expansive on the Valsalva maneuver.
Patient Data
There is a herniation of brain matter (frontal lobe) along with meninges through a midline defect in the frontoethmoidal bone. The swelling lies externally between frontal bone and nasal bone. There is no communication with the ventricles. The remainder brain parenchyma appears normal.
Case Discussion
This case typically illustrates a frontoethmoidal meningoencephalocele. There is herniation of brain matter (frontal lobe) along with meninges through a defect in frontoethmoidal bone. The swelling lies externally between frontal bone and nasal bone leading to nasofrontal type of meningoencephalocele.
Other two types of frontoethmoidal encephaloceles are nasoethmoidal, which exits between the nasal bone and nasal cartilages and naso-orbital, which exits through a defect in the maxillary frontal process. Frontoethmoidal encephaloceles are also known as sincipital encephaloceles.
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