Presentation
Abdominal pain and distension.
Patient Data
Bilateral markedly enlarged both kidneys with near total replacement of their parenchyma by fat containing masses interspersed with solid components consistent with renal angiomyolipomas.
Bi-lobar hepatic few tiny lipomas.
Bilateral cerebral periventricular subependymal calcific nodules, characteristic of tuberous sclerosis.
Case Discussion
This is a unique case of giant renal angiomyolipoma in a known case of tuberous sclerosis. The typical appearance of an AML on CT is a cortical mass containing fat attenuation. The case also shows other characteristic features of tuberous sclerosis such as the bilateral cerebral periventricular subependymal calcifications.