Global cerebellar hypoplasia
Ataxic gait since childhood
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The cerebellum is globally reduced in size with widening of the cerebellar sulci. The supratentorial brain, brainstem and cervical cord appear unremarkable.
The normal shape of the cerebellum with global volume reduction is seen consistent with global cerebellar hypoplasia; a type of congenital morphological cerebellar abnormality. An identical appearance can be seen in diffuse cerebellar atrophy, however, the long-standing history suggests that this is hypoplasia. Only long-term imaging showing stability over extended time can categorically distinguish between these two entities.