Gorham's disease (mandible)

Case contributed by Dr Aditya Shetty

Presentation

Reduced movement of jaw with a dull aching pain associated with a soft tissue swelling.

Patient Data

Age: 5
Gender: Male
X-ray

Absence of mandible is noted

CT

Absence of mandible with a well defined area of collection noted in the soft tissue on the left side

Case Discussion

Case of Gorham's disease involving the mandible 

  • massive osteolysis of mandible with lack of compensatory osteoblastic activity. 
  • replaced by fibrous tissue
  • usually associated with an angiomatous swelling
  • in this case the swelling was due to inflammatory changes proved by an FNAC
  • this disease most commonly involves  the skull, jaw, shoulder, rib cage, and pelvis.
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Case information

rID: 28216
Case created: 15th Mar 2014
Last edited: 1st Oct 2015
Inclusion in quiz mode: Included

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