Gorlin-Goltz syndrome

Case contributed by Dr Dalia Ibrahim


History of multiple maxillary and mandibular cysts. He has undergone a biopsy from the left maxillary cyst.

Patient Data

Gender: Male

Multiple unilocular cysts of variable sizes seen at the mandibular symphysis, body and rami as well as both maxilla, the left maxillary cyst shows internal gas lucency, likely sequel after biopsy.

Calcification of falx cerebri, tentorium and petroclinoid ligaments.

Bilateral maxillary, ethmoidal and frontal sinusitis.

Case Discussion

Biopsy proven odontogenic keratocyte. No evidence of malignancy.

Major criteria of Gorlin-Goltz syndrome

  • basal cell cancers : > 2 or 1 under the age 20
  • odontogenic keratocysts 
  • bilamellar calcification of the falx cerebri
  • palmar pits : 3 or more
  • rib anomalies : bifid rib, fused, splayed
  • first degree relative with Gorlin syndrome

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