Hallervorden-Spatz syndrome

Case contributed by Dr Ashutosh Gandhi

Presentation

c/o dystonia and speech disturbance

Patient Data

Gender: Female
MRI

Bilaterally symmetrical, hyperintense signal changes in the anterior medial globus pallidus, with surrounding hypointensity in the globus pallidus, on T2-weighted scanning. These imaging features are fairly diagnostic of HSD and have been termed the "eye-of-the-tiger" sign.

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Case information

rID: 19830
Case created: 16th Oct 2012
Last edited: 7th Oct 2015
Inclusion in quiz mode: Included

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