Hallervorden Spatz syndrome

Case contributed by Dr Ashutosh Gandhi

Presentation

Dystonia and speech disturbance.

Patient Data

Gender: Female
MRI

Bilaterally symmetrical, hyperintense signal changes in the anterior medial globus pallidus, with surrounding hypointensity in the globus pallidus, on T2-weighted scanning. 

Case Discussion

Imaging features are fairly diagnostic of Hallervorden Spatz syndrome with the specific MRI appearance of "eye of the tiger" sign.

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Case information

rID: 19830
Published: 16th Oct 2012
Last edited: 14th Aug 2019
Inclusion in quiz mode: Included

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