Presentation
Dystonia and speech disturbance.
Patient Data
Gender: Female
From the case:
Pantothenate kinase-associated neurodegeneration
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Bilaterally symmetrical, hyperintense signal changes in the anterior medial globus pallidus, with surrounding hypointensity in the globus pallidus, on T2-weighted scanning.
Case Discussion
Imaging features are fairly diagnostic of pantothenate kinase-associated neurodegeneration with the specific MRI appearance of eye of the tiger sign.