Hallervorden Spatz syndrome

Case contributed by Dr Ashutosh Gandhi


Dystonia and speech disturbance.

Patient Data

Gender: Female

Bilaterally symmetrical, hyperintense signal changes in the anterior medial globus pallidus, with surrounding hypointensity in the globus pallidus, on T2-weighted scanning. 

Case Discussion

Imaging features are fairly diagnostic of Hallervorden Spatz syndrome with the specific MRI appearance of "eye of the tiger" sign.

PlayAdd to Share

Case information

rID: 19830
Published: 16th Oct 2012
Last edited: 14th Aug 2019
Inclusion in quiz mode: Included

Updating… Please wait.

 Unable to process the form. Check for errors and try again.

 Thank you for updating your details.