Hemangioblastoma: von Hippel-Lindau syndrome

Case contributed by A.Prof Frank Gaillard

Patient Data

Age: Young adult
Gender: Male

Cystic lesion with non enhancing walls and vividly enhancing mural nodule in cerebellum: hemangioblastoma

Case Discussion

Final Diagnosis:

Cerebellum: Hemangioblastoma (clinical history of von Hippel-Lindau syndrome).

Microscopic Description:

Sections show the specimen to consist of a vascular tumor associated with small portions of cerebellar tissue. The tumor is characterized by a capillary component, large ectatic vascular structures and cystic elements containing proteinaceous fluid. These structures are within a stromal tumor background composed of clear cells with small round nuclei. In areas, focal permeation into cerebellar tissue is observed.

PlayAdd to Share

Case information

rID: 4314
Published: 7th Aug 2008
Last edited: 23rd Jun 2016
Inclusion in quiz mode: Included

Updating… Please wait.

 Unable to process the form. Check for errors and try again.

 Thank you for updating your details.