Hereditary angioedema (small bowel)

Case contributed by A.Prof Frank Gaillard

Presentation

Abdominal pain.

Patient Data

Age: 55 year
Gender: Male
CT

CT abdomen

Approximately 30-40 cm length of mid small bowel at the right abdomen demonstrates smooth, low density mural thickening with abrupt transition to normal bowel thickness. Associated surrounding fat stranding and moderate volume of mesenteric and free intraperitoneal fluid, with fluid tracking into the right inguinal canal. No mechanical obstructing lesion identified. The terminal ileum and adjacent ascending colon are normal. No filling defect within the superior mesenteric artery or vein.

Case Discussion

Approximately 30-40 cm length of small bowel mural thickening is nonspecific, and is compatible with angioedema of the small bowel given the clinical history of hereditary angioedema.

Differentials include infectious, inflammatory and less likely ischaemic aetiologies.

The patient spontaneously recovered although he has had repeated admissions with abdominal pain.

PlayAdd to Share

Case information

rID: 16239
Case created: 2nd Jan 2012
Last edited: 26th Dec 2015
Inclusion in quiz mode: Included

Updating… Please wait.
Loadinganimation

Alert accept

Error Unable to process the form. Check for errors and try again.

Alert accept Thank you for updating your details.