Hereditary haemorrhagic telangiectasia (possible)

Case contributed by Dr Maulik S Patel

Presentation

Vague abdominal discomfort for 3 -4 mths.

Patient Data

Age: about 50 yrs
Gender: Male

Multiple images of liver.

LIVER  is normal in  size. Mild coarsening of echopattern is noted without surface nodularity / capsular loss.

Diffuse dilatation main hepatic artery and its intrahepatic branches is noted.

Main hepatic artery - diameter of 11 mm.  No thrombus is noted.

Increased intrahepatic vascularity is noted.

No solid or cystic mass lesion is seen.

Intrahepatic biliary redicles are not dilated. Portal and hepatic veins are patent.

Case Discussion

Ultrasound features of diffuse dilatation of hepatic artery and its braches.

A leading question of epistaxis was asked and there was positive history for long term.

Possibility of Hereditary haemorrhagic telangiectasia was suggest in view of ultrasound findings and clinical back ground.

CT scan done later ( No copy right, not uploaded ) -  Dilated hepatic artery, Bilateral lung base vascular anomalies.  Intraluminal polypoid lesion in caecum. 

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Case information

rID: 27720
Case created: 16th Feb 2014
Last edited: 18th Dec 2015
Inclusion in quiz mode: Included

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