Herlyn-Werner-Wunderlich syndrome

Case contributed by Dr Dalia Ibrahim

Presentation

Left pelvic pain.

Patient Data

Age: 20-year-old
Gender: Female
Modality: CT

Complete duplication of uterine horns as well as duplication of the cervix and vagina. 

 The right hemivagina appears collapsed.

The left hemivagina appears distended by fluid like density; likely obstructed left hemivagina, secondary to vaginal septum.

Absent left kidney (at the same side of vaginal obstruction)

Modality: Annotated image

Complete duplication of uterine horns as well as duplication of the cervix and vagina. 

 The right hemivagina appears collapsed.

The left hemivagina appears distended by fluid like density; likely obstructed left hemivagina, secondary to vaginal septum.

Absent left kidney (at the same side of vaginal obstruction).

Case Discussion

Herlyn-Werner-Wunderlich (HWW) syndrome is a very rare congenital anomaly of the urogenital tract involving Müllerian ducts and Wolffian structures,

It is characterized by the triad of:

  • Duplication of the uterus, cervix and vagina
  • Unilateral haematocolpos or haematometrocolpos
  • Absent kidney on the same side as the uterovaginal obstruction
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Case Information

rID: 29052
Case created: 29th Apr 2014
Last edited: 7th Dec 2016
System: Gynaecology
Inclusion in quiz mode: Included

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