Herlyn-Werner-Wunderlich syndrome

Case contributed by Dr Mustafa Hammad

Presentation

23 year old female, complains of infertility, came to ER due to pelvic pain.

Patient Data

Age: 23 years
Gender: Female

Two uterine horns, two cervical canals and two vaginas are seen with retained fluid intensity with blood products noted within the left vaginal canal denoting hematocolpos, while the right uterine horn is within normal. There is also a right ovarian simple cyst.

Ultrasound

Absent left kidney, with compensatory enlargement of the right kidney, which measures approximately 14 cm.

Case Discussion

Herlyn–Werner–Wunderlich syndrome is considered to be a rare type of Mullerian duct anomaly, it is characterised by uterus didelphys with blind hemivagina and associated ipsilateral renal agenesis.

Herlyn–Werner–Wunderlich syndrome is also known obstructed hemivagina, and ipsilateral renal anomaly (OHVIRA). It usually presents after menarche, with progressive pelvic pain during menses secondary to haematocolpos, so early diagnosis can help early treatment, ensure quick relief from symptoms and preserve the fertility and so prevent the complications.

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Case information

rID: 47168
Case created: 2nd Aug 2016
Last edited: 20th Nov 2016
Inclusion in quiz mode: Excluded

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