Heterotaxy Syndrome
Diagnosis certain
Disclosures
- updated 8 Sep 2022:
Nothing to disclose
Updates to Case Attributes
Body
was changed:
Heterotaxy syndrome (situs ambiguous) is a disturbance in the usual left-right distribution of the thoracoabdominal organs. Unlike situs inversus, heterotaxy does not entirely translate into a complete mirror image. This syndrome can be disturbed into one of two subsets:
1.) heterotaxy heterotaxy with isomerism of the right atrial appendages (asplenia syndrome)
2.) heterotaxy heterotaxy with isomerism of the left atrial appendages (polysplenia syndrome)
-<p>Heterotaxy syndrome (situs ambiguous) is a disturbance in the usual left-right distribution of the thoracoabdominal organs. Unlike situs inversus, heterotaxy does not entirely translate into a complete mirror image. This syndrome can be disturbed into one of two subsets:</p><p>1.) heterotaxy with isomerism of the right atrial appendages (asplenia syndrome)</p><p>2.) heterotaxy with isomerism of the left atrial appendages (polysplenia syndrome)</p>- +<p>Heterotaxy syndrome (situs ambiguous) is a disturbance in the usual left-right distribution of the thoracoabdominal organs. Unlike situs inversus, heterotaxy does not entirely translate into a complete mirror image. This syndrome can be disturbed into one of two subsets:</p><p>1. heterotaxy with isomerism of the right atrial appendages (asplenia syndrome)</p><p>2. heterotaxy with isomerism of the left atrial appendages (polysplenia syndrome)</p>