Heterotaxy Syndrome

Changed by Fabio Macori on 21 Sep 15:33
Diagnosis certain
Disclosures - updated 8 Sep 2022: Nothing to disclose

Updates to Case Attributes

Body was changed:

Heterotaxy syndrome (situs ambiguous) is a disturbance in the usual left-right distribution of the thoracoabdominal organs. Unlike situs inversus, heterotaxy does not entirely translate into a complete mirror image. This syndrome can be disturbed into one of two subsets:

1.) heterotaxy heterotaxy with isomerism of the right atrial appendages (asplenia syndrome)

2.) heterotaxy heterotaxy with isomerism of the left atrial appendages (polysplenia syndrome)

  • -<p>Heterotaxy syndrome (situs ambiguous) is a disturbance in the usual left-right distribution of the thoracoabdominal organs. Unlike situs inversus, heterotaxy does not entirely translate into a complete mirror image. This syndrome can be disturbed into one of two subsets:</p><p>1.) heterotaxy with isomerism of the right atrial appendages (asplenia syndrome)</p><p>2.) heterotaxy with isomerism of the left atrial appendages (polysplenia syndrome)</p>
  • +<p>Heterotaxy syndrome (situs ambiguous) is a disturbance in the usual left-right distribution of the thoracoabdominal organs. Unlike situs inversus, heterotaxy does not entirely translate into a complete mirror image. This syndrome can be disturbed into one of two subsets:</p><p>1. heterotaxy with isomerism of the right atrial appendages (asplenia syndrome)</p><p>2. heterotaxy with isomerism of the left atrial appendages (polysplenia syndrome)</p>

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