Hirayama disease

Case contributed by Dr Prashant Gupta

Presentation

Bilateral upper limb weakness

Patient Data

Age: 20
Gender: Male
Modality: MRI

Case Discussion

Hirayama disease is a form of muscular dystrophy seen in 2nd-3rd decade. It is thought to be due to disproportionate growth between canal contents and bony spinal canal resulting in a lax dura in extension and vice versa.

Contrast MRI may be done to demonstrate findings better but is not essential. A dynamic MRI should definitely be done in every suspected case.

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Case Information

rID: 17260
Case created: 30th Mar 2012
Last edited: 15th Dec 2015
Inclusion in quiz mode: Included

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