Hirayama disease

Case contributed by Utkarsh Kabra
Diagnosis almost certain

Presentation

Unilateral upper limb weakness with wasting of muscles of hand.

Patient Data

Age: 18 years
Gender: Male
mri

Atrophy of cord is seen with reduced AP diameter from C5-6 to C6-7 levels. On flexion, anterior displacement of posterior dura is seen with significant prominence of posterior epidural space.

No convincing intramedullary hyperintensity is, however, seen in present scan.

Case Discussion

In the given clinical context, the findings are suggestive of Hirayama disease.

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