Presentation
Bilateral hand muscle wasting.
Patient Data
Age: 30 years
Gender: Male
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Cervical spine MRI images in the neutral position show marked lower cervical cord atrophy with some linear high T2 cord signal.
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MRI cervical spine images in the flexed position demonstrate anterior displacement of the dura from C4 to T1 with expanded enhancing posterior epidural space. Cord atrophy due to this phenomenon is known as Hirayama disease.
Case Discussion
Marked lower cervical cord atrophy which is confirmed on post contrast flexion imaging to be due to Hirayama disease. This disease classically presents with bilateral forearm and hand muscle wasting.