Hirayama disease

Case contributed by Dr Andrew Dixon

Presentation

Bilateral hand muscle wasting.

Patient Data

Age: 30
Gender: Male

MRI Cervical Spine (neutral position)

Modality: MRI

Cervical spine MRI images in the neutral position show marked lower cervical cord atrophy with some linear high T2 cord signal.

MRI Cervical Spine (flexed position)

Modality: MRI

MRI cervical spine images in the flexed position demonstrate anterior displacement of the dura from C4 to T1 with expanded enhancing posterior epidural space. Cord atrophy due to this phenomenon is known as Hirayama disease

Case Discussion

Marked lower cervical cord atrophy which is confirmed on post contrast flexion imaging to be due to Hirayama disease. This disease classically presents with bilateral forearm and hand muscle wasting.

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Case Information

rID: 18088
Case created: 7th Jun 2012
Last edited: 6th Nov 2016
Inclusion in quiz mode: Included

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