Hirayama disease

Case contributed by Dr Andrew Dixon


Bilateral hand muscle wasting.

Patient Data

Age: 30
Gender: Male

MRI Cervical Spine (neutral position)

Cervical spine MRI images in the neutral position show marked lower cervical cord atrophy with some linear high T2 cord signal.


MRI Cervical Spine (flexed position)

MRI cervical spine images in the flexed position demonstrate anterior displacement of the dura from C4 to T1 with expanded enhancing posterior epidural space. Cord atrophy due to this phenomenon is known as Hirayama disease

Case Discussion

Marked lower cervical cord atrophy which is confirmed on post contrast flexion imaging to be due to Hirayama disease. This disease classically presents with bilateral forearm and hand muscle wasting.

PlayAdd to Share

Case information

rID: 18088
Published: 7th Jun 2012
Last edited: 16th Jul 2018
Inclusion in quiz mode: Included

Updating… Please wait.

 Unable to process the form. Check for errors and try again.

 Thank you for updating your details.