Hirayama disease

Case contributed by A.Prof Frank Gaillard

Presentation

10 months of right arm weakness.

Patient Data

Age: 20 years
Gender: Male
Modality: MRI

In neutral position the canal is capacious and no neural exit foraminal stenosis is present. The cord is essentially unremarkable in appearance, although does appear perhaps slightly thinned at the C5/6 level without convincing cord signal abnormality. During flexion there is anterior displacement of the posterior theca such that it compresses the cord between it and the spinal column anteriorly at C5/6. The epidural venous space dorsal to the theca expands to over 6 mm in depth.  

Case Discussion

Features are consistent with and characteristic of Hirayama disease, which is an easily overlooked diagnosis if not suspected. 

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Case Information

rID: 21940
Case created: 28th Feb 2013
Last edited: 2nd Nov 2015
Tag: spine
Inclusion in quiz mode: Included

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