Presentation
Long standing constipation since early childhood.
Patient Data
Age: 8 years
Gender: Male
From the case:
Hirschsprung disease
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Small caliber of the distal rectum with proximal dilatation. Fasciculation of the aganglionic segment is seen.
From the case:
Hirschsprung disease
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Significantly dilated colons with collapsed rectum. The transitional zone can be appreciated in all axial, coronal and sagittal planes. The rectosigmoid ratio is completely obliterated.
Case Discussion
Commonly a short segment of aganglionic distal colon/rectum is responsible for the disease. A late presentation like this case can result in significant proximal dilatation.