Hypoplastic right heart syndrome

Case contributed by Tudonyang Kibet Denis


Routine anomaly scan at 18 weeks gestation. 11-13 weeks scan was not performed.

Patient Data

Age: 30 years
Gender: Female

Situs solitus.

Atretic right ventricle with intact interventricular septum.

Tricuspid and pulmonary valve atresia.

Absent right atrioventricular flow on color Doppler.

Additional A wave reversal was demonstrated in the ductus venosus spetral waveform.

Case Discussion

Hypoplastic right heart syndrome (HRHS) is a rare congenital cardiac anomaly that presents with underdevelopment of the right ventricle.

It is usually associated with pulmonary atresia, tricuspid atresia and septal defects.

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