Intussusception secondary to Peutz-Jeghers syndrome

Case contributed by Alex Pearce

Presentation

Background of Peutz-Jeghers syndrome presents with acute abdominal pain and symptoms of bowel obstruction

Patient Data

Age: 30 years
Gender: Female

There is very marked thickening of one of the proximal loops of small bowel in the left upper quadrant extending down the left side of the abdomen with very marked localized dilatation.

The appearances suggest jejunal intussusception which is a recognized complication of this syndrome.

Stomach is normal in appearance and the duodenum is not dilated at this stage.

The liver is normal in appearance. There is a degree of splenomegaly.

The pancreas, kidneys and adrenals appear normal.

Conclusion: Appearances suggest intussusception of one of the loops of proximal small bowel complicating this polyposis syndrome, with resultant marked localized dilatation.

Case Discussion

Patient underwent successful proximal small bowel resection, with two palpable intra-luminal tumors identified in the jejunum. Intussusception appears as a soft-tissue mass composed of a central intussusceptum and outer intussuscipiens. 

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Case information

rID: 74166
Published: 15th Feb 2020
Last edited: 14th Jun 2021
Inclusion in quiz mode: Included
Institution: Northern beaches

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