Intussusception secondary to Peutz-Jeghers syndrome
Background of Peutz-Jeghers syndrome presents with acute abdominal pain and symptoms of bowel obstruction
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There is very marked thickening of one of the proximal loops of small bowel in the left upper quadrant extending down the left side of the abdomen with very marked localized dilatation.
The appearances suggest jejunal intussusception which is a recognized complication of this syndrome.
Stomach is normal in appearance and the duodenum is not dilated at this stage.
The liver is normal in appearance. There is a degree of splenomegaly.
The pancreas, kidneys and adrenals appear normal.
Conclusion: Appearances suggest intussusception of one of the loops of proximal small bowel complicating this polyposis syndrome, with resultant marked localized dilatation.
Patient underwent successful proximal small bowel resection, with two palpable intra-luminal tumors identified in the jejunum. Intussusception appears as a soft-tissue mass composed of a central intussusceptum and outer intussuscipiens.