Isolated left-sided pulmonary artery agenesis with left lung hypoplasia
Presentation
Respiratory distress. Chest x-ray (not shown) shows opaque left hemithorax.
Patient Data
Absence of the left pulmonary artery.
Decrease volume of the left lung with mild mediastinum deviation to the left side.
Normal main pulmonary artery and right pulmonary artery.
Normal trachea and both main bronchi.
Case Discussion
Unilateral absence of pulmonary artery is a rare anomaly and usually presents in children and adults with respiratory distress. It may be associated with cardiovascular anomalies like coarctation of the aorta, VSD, ASD, and tetralogy of Fallot. Chest x-ray usually demonstrates volume loss of the affected side with an ipsilateral mediastinal shift, but the diagnosis is established by imaging methods like CT angiography and MRI.
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